Silence after the storm; a case report on Bickerstaff Brainstem encephalitis

Authors : Emine TEKİN, Turgay ÇOKYAMAN, Haydar Ali  TAŞDEMİR, Hamit ÖZYÜREK

Pages : 341-344

Doi:10.12956/tchd.772099

View : 17 | Download : 6

Publication Date : 2021-07-16

Article Type : Other Papers

Abstract :A pediatric case with Bickerstaff’s brainstem encephalitis insert ignore into journalissuearticles values(BBE);, which is a very rare monophasic post-infectious condition characterized by central nervous system involvement, unconsciousness, ophthalmoplegia and ataxia, is presented. Twelve years old patient was brought with difficulty in eye movements and ataxia. On the second day, she became agitated and lethargic, and then bulbar palsy and whole body paralysis developed. Upper motor neuron involvement was evident. Routine biochemical parameters and serologic tests, cranial magnetic resonance imaging, lumbar puncture, autoimmune, paraneoplastic, and electrophysiological studies were evaluated. All were normal except for the encephalopathic first electroencephalography insert ignore into journalissuearticles values(EEG); and the EEG repeated on the 25th day was reported to be normal. Anti-ganglioside antibody, anti-GQ1b was found positive. Intravenous immunoglobulin insert ignore into journalissuearticles values(IVIG); started on the fourth day. A very rapid improvement was seen in the first week of IVIG treatment. She was able to walk in the second week. She was completely normal in 3 months. Although seven years passed, our patient has not had any relapse or neurological deficit. We presented a case diagnosed as BBE treated successfully with single dose intravenous Immunoglobulin. We wanted to emphasize that BBE has a good prognosis even though it is an acutely developing severe condition.
Keywords : Ataksi, Bickerstaff beyin sapı, Ensefaliti, İntravenous immunoglobulin