Caroli`s syndrome associated with polycystic kidney disease

Authors : B. Altuntaş, N. Yaralı, S. KARAYALÇIN, S. KUYUCU, N. ARDA, A. AKÇAYOZ, Z. ARSLAN, Ü. ERTAN, A. ÖNER, T. TEZİÇ

Pages : 206-210

View : 8 | Download : 4

Publication Date : 1997-10-01

Article Type : Research Paper

Abstract :Congenital intrahepatic biliary duct dilatation associated with congenital hepatic fibrosis insert ignore into journalissuearticles values(CHF);, referred to as Caroli`s syndrome, is a rare condition. Caroli`s syndrome is generally associated with autosomal recessive polycystic kidney disease insert ignore into journalissuearticles values(ARPKD); or rarely autosomal dominant polycystic kidney disease insert ignore into journalissuearticles values(ADPKD);. in this case report, we describe a thirteen and a nine- year-old two brothers with Caroli`s syndrome and polycystic kidney disease. There was no parental consanguinity. The elder brother had a history of jaundice. However, the little one had only a history of periodic abdominal pain and on follow up, he had acute pyelonephritis.
Keywords : Caroli`s Syndrome, poliycystic kidney disease, children, acute pyelonephritis