Joubert Sendromlu Hastanın Skolyoz Cerrahisinde Anestezi Yönetimi: Olgu Sunumu

Authors : Mehmet Bilhan HAYIRLIOĞLU, Banu Gökay VURAL, Müzeyyen İYİGÜN, Tayfun GÜLER

Pages : 110-112

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Publication Date : 2019-03-01

Article Type : Other Papers

Abstract :Joubert Syndrome is a rare, autosomal recessive AR disorder characterized byneurologic findings as hypotonia, ataxia, physhcomotor developmental delay, abnormal respiratory pattern and abnormal eye movements. Molar tooth sign caused by cerebellar vermis hypoplasia is a neuroradiologic diagnostic criteria in cranial magnetic resonance imaging MRI . Scolisosis is common in these patients due to hypotonia during the early developmental period. In this article we presented our anesthesia management during scoliosis correction surgery in a patient with Joubert Syndrome
Keywords : Joubert syndrome, scoliosis, pediatric anesthesia, neurophysiological monitoring, neuromonitoring