Botyroid Rhabdomyosarcoma of the Vagina in A Two-month-old Girl

Authors : Defne Ay Tuncel, Ayşe Yiğit Sönmez, Fulya Adamhasan

Pages : 143-145

Doi:10.17517/ksutfd.1187920

View : 22 | Download : 44

Publication Date : 2024-03-28

Article Type : Other Papers

Abstract :Botyroid rhabdomyosarcoma is the most common malignant mesencymal tumor of the vagina in children and infants. It is a malignant tumor that arises from immature skeletal muscle cells (i.e., rhabdomyoblasts) lining the walls of hollow organs, including the vagina, bladder, and biliary tract. This cancer most commonly affects children under the age of 4, although it can sometimes present in older individuals. Botyroid sarcoma is usually found in the vagina during infancy and early childhood, in the cervix during reproductive years, and in the corpus uteri during postmenapausal years. Treatment is combination of surgery with adjuvants chemotherapy and radiotherapy. We report a case of two-month-old girl presented with a history of vaginal bleeding and a mass protruding from vagina. Diffusion Magnetic Resonance Imaging (MRI) showed an approximately 6 cm mass in rectovaginal septum. Excisional biopsy from the vagina confirmed the diagnosis of botyroid rhabdomyosarcoma. After biopsy the patient received multiple cycles of chemotherapy. The patient is disease-free on remission at this time.
Keywords : Botryoid, rabdomyosarkom, vajina, tümör